Muscle strengthening intervention for boys with haemophilia: Developing and evaluating a best-practice exercise programme with boys, families and health-care professionals

Journal article

Hashem, F., Stephensen, D., Drechsler, W.I., Bladen, M., Carroll, L., Pellatt-Higgins, T. and Saloniki, E.C. 2020. Muscle strengthening intervention for boys with haemophilia: Developing and evaluating a best-practice exercise programme with boys, families and health-care professionals. Health Expectations. 23 (5), pp. 1350-1361. https://doi.org/10.1111/hex.13119
AuthorsHashem, F., Stephensen, D., Drechsler, W.I., Bladen, M., Carroll, L., Pellatt-Higgins, T. and Saloniki, E.C.
Abstract

Background: Muscle strengthening exercises have the potential to improve outcomes for boys with haemophilia, but it is unclear what types of exercise might be of benefit.
We elicited the views of health-care professionals, boys and their families to create and assess a home-based muscle strengthening programme.

Objective: To design and develop a muscle strengthening programme with healthcare professionals aimed at improving musculoskeletal health, and refine the intervention by engaging boys with haemophilia and their families (Study 1). Following delivery, qualitatively evaluate the feasibility and acceptability of the exercise programme with the boys and the study's physiotherapists (Study 2). Design: A person-based approach was used for planning and designing the exercise programme, and evaluating it post-delivery. The following methods were utilized: modified nominal group technique (NGT) with health-care professionals; focus group with families; exit interviews with boys; and interviews with the study's physiotherapists.

Results: Themes identified to design and develop the intervention included exercises to lower limb and foot, dosage, age accommodating, location, supervision and
monitoring and incentivization. Programme refinements were carried out following engagement with the boys and families who commented on: dosage, location, supervision
and incentivization. Following delivery, the boys and physiotherapists commented on progression and adaptation, physiotherapist contact, goal-setting, creating
routines and identifying suitable timeframes, and a repeated theme of incentivization.

Conclusions: An exercise intervention was designed and refined through engagement with boys and their families. Boys and physiotherapists involved in the intervention's delivery were consulted who found the exercises to be generally acceptable with some minor refinements necessary.

KeywordsBoys; Exercise; Haemophilia; Life-experience; Muscle strength; Patient adherence; Physiotherapy
Year2020
JournalHealth Expectations
Journal citation23 (5), pp. 1350-1361
PublisherWiley
ISSN1369-6513
1369-7625
Digital Object Identifier (DOI)https://doi.org/10.1111/hex.13119
Official URLhttps://onlinelibrary.wiley.com/doi/10.1111/hex.13119
FunderNational Institute for Health and Care Research (NIHR)
Publication dates
Online17 Aug 2020
Publication process dates
Accepted21 Jul 2020
Deposited31 Mar 2022
Publisher's version
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Open
Output statusPublished
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